Successful surgical treatment of Bland - White -Garland syndrome in an adult patient
https://doi.org/10.24884/0042-4625-2020-179-1-69-73
Abstract
Bland - White - Garland syndrome (BWGS) is a clinical symptom complex, which is based on the congenital anomalous discharge of the left coronary artery of the heart from the pulmonary trunk. This article presents a case report of successful surgical treatment of BWGS in an adult patient (25 years). The patient after childbirth began to note fatigue, angina pectoris, dyspnea, heartbeat with rapid walking up to 100 meters. The patient underwent coronary angiography, echocardiography, multispiral computed tomography. As a result of researches, it was established abnormal discharge of the left coronary artery from the pulmonary trunk. Surgical treatment was performed - reimplantation of the main left coronary artery into the aorta with repair of the pulmonary trunk with xenopericardium. Discharged on the 16th day after surgery.
About the Authors
S. A. Belash
Scientific Research Institute - Ochapovsky Regional Clinical Hospital № 1; Kuban State Medical University
Russian Federation
Competing Interests:
Russian Federation
Belash Sergey A. - Cand. of Sci. (Med.), cardiovascular surgeon of Department Adult Cardiosurgery № 2, Research Institute - Ochapovskiy Regional Clinical Hospital № 1; assistant of Department of Cardiac Surgery and Cardiology, Kuban State Medical University.
Krasnodar.
Competing Interests:
The authors declare no conflict of interest.
K. O. Barbukhatti
Scientific Research Institute - Ochapovsky Regional Clinical Hospital № 1; Kuban State Medical University
Russian Federation
Competing Interests:
Russian Federation
Barbukhatti Kirill O. - Dr. of Sci. (Med.), Professor, chief of Department Adult Cardiosurgery № 2, Research Institute - Ochapovskiy Regional Clinical Hospital № 1; chief of department of Cardiac Surgery and Cardiology, Kuban State Medical University.
Krasnodar.
Competing Interests:
The authors declare no conflict of interest.
E. P. Yasakova
Scientific Research Institute - Ochapovsky Regional Clinical Hospital № 1
Russian Federation
Competing Interests:
Russian Federation
Yasakova Elena P. - radiologis of Department of Radiation Diagnostics, Research Institute - Ochapovskiy Regional Clinical Hospital № 1.
167, 1 May str., Krasnodar, 350086.
Competing Interests:
The authors declare no conflict of interest.
M. M. Amary
Kuban State Medical University
Russian Federation
Competing Interests:
Russian Federation
Amary Mary M. - cardiovascular surgeon of Department Adult Cardiosurgery № 2, Research Institute - Ochapovskiy Regional Clinical Hospital № 1.
167, 1 May str., Krasnodar, 350086.
Competing Interests:
The authors declare no conflict of interest.
V. A. Porhanov
Scientific Research Institute - Ochapovsky Regional Clinical Hospital № 1
Russian Federation
Competing Interests: The authors declare no conflict of interest.
Russian Federation
Porhanov Vladimir A. - Professor, academician of RAS, director, Research Institute - Ochapovskiy Regional Clinical Hospital № 1; chief of department of Oncology and Thoracic Surgery, Kuban State Medical University.
Krasnodar.
Competing Interests: The authors declare no conflict of interest.
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Review
For citations:
Belash S.A., Barbukhatti K.O., Yasakova E.P., Amary M.M., Porhanov V.A. Successful surgical treatment of Bland - White -Garland syndrome in an adult patient. Grekov's Bulletin of Surgery. 2020;179(1):69-73. (In Russ.) https://doi.org/10.24884/0042-4625-2020-179-1-69-73
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