Features of diagnosis and surgical treatment of a patient with multiple endocrine neoplasia type 1
https://doi.org/10.24884/0042-4625-2023-182-6-36-43
Abstract
A clinical case of examination and treatment of a 29-year-old female patient with type 1 multiple endocrine neoplasia with calcitonin-secreting pancreatic tumors is presented. The difficulties of modern complex diagnostics are shown, as well as the effectiveness of multi-stage surgical tactics involving specialists of various profiles. The conducted laboratory and instrumental examination, which included the entire arsenal of high-tech methods, made it possible to timely diagnose a combined lesion of several endocrine organs. Based on the assessment of the functional activity of the identified tumors, the order of the stages of surgical treatment was substantiated. The implementation of the proposed surgical tactics contributed to the normalization of the patient’s hormonal status and improved quality of life.
About the Authors
P. N. Romashchenko
Military Medical Academy
Russian Federation
Russian Federation
Romashchenko Pavel N., Dr. of Sci. (Med.), Professor, Corresponding Member of the RAS, Head of the Department and Clinic of Faculty Surgery named after S.P. Fedorov
Saint Petersburg
N. A. Maistrenko
Military Medical Academy
Russian Federation
Russian Federation
Maistrenko Nicolay А., Dr. of Sci. (Med.), Professor, Academician of the RAS, Professor of the Department and Clinic of Faculty Surgery named after S.P. Fedorov
Saint Petersburg
D. S. Krivolapov
Military Medical Academy
Russian Federation
Russian Federation
Krivolapov Denis S., Cand. of Sci. (Med.), Teacher of the Department and Clinic of Faculty Surgery named after S.P. Fedorov
Saint Petersburg
E. B. Kireeva
Military Medical Academy
Russian Federation
Russian Federation
Kireeva Elena B., Cand. of Sci. (Med.), Associate Professor, Honored Doctor of the Russian Federation, Head of the Department of Outpatient Care
Saint Petersburg
M. S. Simonova
Military Medical Academy
Russian Federation
Russian Federation
Simonova Maria S., Сlinical Resident of the Department and Clinic of Faculty Surgery named after S.P. Fedorov
6, Academika Lebedeva str., Saint Petersburg, 194044
A. K. Aliev
Military Medical Academy
Aliev Arsen K., Cand. of Sci. (Med.), Associate Professor of the S.P. Fedorov Department and Clinic of Faculty Surgery
Saint Petersburg
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Romashchenko P.N., Maistrenko N.A., Krivolapov D.S., Kireeva E.B., Simonova M.S., Aliev A.K. Features of diagnosis and surgical treatment of a patient with multiple endocrine neoplasia type 1. Grekov's Bulletin of Surgery. 2023;182(6):36-43. (In Russ.) https://doi.org/10.24884/0042-4625-2023-182-6-36-43
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