A rare case of surgical treatment of a patient with gastric cancer with Cartagener syndrome
S. G. Afanasyev,
A. Yu. Dobrodeev,
D. N. Kostromitsky,
Yu. V. Rudyk,
M. Yu. Grishchenko,
E. S. Drozdov,
E. N. Samtsov,
U. B. Urmonov https://doi.org/10.24884/0042-4625-2020-179-5-91-94
Abstract
Kartagener Syndrome (CS) is a rare autosomal recessive disease that is a part of primary ciliary dyskinesia (PCD), and is characterized by a triad of syndrome including bronchiectasis, polysinusitis and a complete mirror arrangement of the internal organs of the chest and abdominal cavities (situs inversus). In most patients, bronchiectasis in the lungs develops from the first years of life and progresses in time. The tardy diagnostic leads to a poor prognosis of the disease and adduce the development of persistent violations of the function of external respiration. Most often, patients with CS are observed by physicians and pulmonologists from early childhood, since respiratory infections often require annual hospitalization in specialized medical institutions due to abnormalities of the ciliary epithelium of the respiratory tract. However, to date, there are no generally accepted recommendations for the management and treatment of patients in this category. This article describes the case of a newly diagnosed CS in an older patient undergoing surgical treatment for gastric cancer. Despite the pronounced concomitant pathology on the part of the bronchopulmonary system, the perioperative period in the patient proceeded relatively satisfactorily and did not entail an increase in the length of hospitalization.
About the Authors
S. G. Afanasyev
Tomsk National Research Medical Center of the Russian Academy of Sciences
Russian Federation
Russian Federation
Dr. of Sci. (Med.), Professor, Head of the Department of Abdominal Oncology, Research Institute of Oncology,
Tomsk
A. Yu. Dobrodeev
Tomsk National Research Medical Center of the Russian Academy of Sciences
Russian Federation
Russian Federation
Dr. of Sci. (Med.), Leading Research Fellow of the Department of Abdominal Oncology, Research Institute of Oncology,
Tomsk
D. N. Kostromitsky
Tomsk National Research Medical Center of the Russian Academy of Sciences;
Tomsk Regional Oncology Hospital
Russian Federation
Russian Federation
Cand. of Sci. (Med.), Junior Research Fellow of the Department of Abdominal Oncology, Research Institute of Oncology,
Tomsk
Yu. V. Rudyk
Tomsk Regional Oncology Hospital
Russian Federation
Russian Federation
Cand. of Sci. (Med.), Oncologist of the Oncology Department,
Tomsk
M. Yu. Grishchenko
Tomsk Regional Oncology Hospital
Russian Federation
Russian Federation
Cand. of Sci. (Med.), Head of the Oncology Department,
Tomsk
E. S. Drozdov
Tomsk Regional Oncology Hospital
Russian Federation
Russian Federation
Cand. of Sci. (Med.), Oncologist of the Oncology Department,
Tomsk
E. N. Samtsov
Tomsk National Research Medical Center of the Russian Academy of Sciences
Russian Federation
Russian Federation
Dr. of Sci. (Med.), Radiologist of the Department of Radiation Diagnostic Methods, Research Institute of Oncology,
Tomsk
U. B. Urmonov
Tomsk National Research Medical Center of the Russian Academy of Sciences
Russian Federation
Russian Federation
Postgraduate Student of the Department of Abdominal Oncology, Research Institute of Oncology,
Tomsk
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For citations:
Afanasyev S.G., Dobrodeev A.Yu., Kostromitsky D.N., Rudyk Yu.V., Grishchenko M.Yu., Drozdov E.S., Samtsov E.N., Urmonov U.B. A rare case of surgical treatment of a patient with gastric cancer with Cartagener syndrome. Grekov's Bulletin of Surgery. 2020;179(5):91-94. (In Russ.) https://doi.org/10.24884/0042-4625-2020-179-5-91-94
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