Diagnostic difficulties and treatment features of a patient with presacral myelolipoma
https://doi.org/10.24884/0042-4625-2025-184-3-95-99
Abstract
Myelolipoma is a benign mesenchymal tumor composed of mature fat and hematopoietic cells in its histological structure. Most often, they are solitary and non-functioning neoplasms. The incidence occurs in the fifth and sixth decades of life. Most often, these tumors are found in the adrenal glands. A rarer situation is when myelolipomas occur in other various parts of the body. Sometimes they are found in the pelvic cavity, chest, retroperitoneal space and some other areas of the human body. The clinically myelolipomas of various localizations remains unclearly. They are often discovered accidentally during computer tomography (CT) for other diseases. Thus, due to the fat content in the histological composition, these formations are interpreted as liposarcomas when performing visualization methods of research. Works devoted to the diagnosis of extra-adrenal myelolipomas due to their rarity are few, while even less is devoted to the treatment of such formations. The article describes a clinical case of diagnosis of extra-adrenal myelolipoma of the presacral space, diagnosed on positron emission computed tomography (PET-CT) as liposarcoma, as well as the features of its minimally invasive surgical treatment.
About the Authors
B. V. SiguaRussian Federation
Sigua Badri V., Dr. of Sci. (Med), Professor of the Department of Faculty Surgery with the Course of Endoscopy named after I. I. Grekov
Competing Interests:
The authors declare no conflict of interest.
E. A. Zakharov
Russian Federation
Zakharov Evgeni A., Cand. of Sci. (Med), Assistant of the Department of Faculty Surgery with the Course of Endoscopy named after I. I. Grekov
Competing Interests:
The authors declare no conflict of interest.
E. L. Latariya
Russian Federation
Latariya Elgudzha L., Cand. of Sci. (Med), Associate Professor of the Department of Faculty Surgery with the Course of Endoscopy named after I. I. Grekov
Competing Interests:
The authors declare no conflict of interest.
O. B. Tcelykovskaia
Russian Federation
Tcelykovskaia Olesya B., Resident of the Department of Faculty Surgery with the Course of Endoscopy named after I. I. Grekov
Competing Interests:
The authors declare no conflict of interest.
A. A. Kurkov
Russian Federation
Kurkov Alexey A., Cand. of Sci. (Med), Assistant of the Department of Faculty Surgery with the Course of Endoscopy named after I. I. Grekov, Head of Surgical Department № 2
Competing Interests:
The authors declare no conflict of interest.
D. G. Berest
Russian Federation
Berest Dmitriy G., Cand. of Sci. (Med), Associate Professor of the Department of Faculty Surgery with the Course of Endoscopy named after I. I. Grekov, Head of Endoscopic Department
Competing Interests:
The authors declare no conflict of interest.
E. E. Leenman
Russian Federation
Leenman Elena E., Cand. of Sci. (Med), Pathologist of the Pathoanatomical Department of Clinical Molecular Morphology at the Clinic named after E.E. Eichwald
Competing Interests:
The authors declare no conflict of interest.
S. A. Vinnichuk
Russian Federation
Vinnichuk Sergey A., Cand. of Sci. (Med), Associate Professor of the Department of Pathological Anatomy, Head of Central Pathoanatomical Department
Competing Interests:
The authors declare no conflict of interest.
V. P. Zemlyanoy
Russian Federation
Zemlyanoy Vyasheslav P., Dr. of Sci. (Med), Professor, Head of the Department of Faculty Surgery with the Course of Endoscopy named after I. I. Grekov, Director of the Institute of Surgery
Competing Interests:
The authors declare no conflict of interest.
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Supplementary files
Review
For citations:
Sigua B.V., Zakharov E.A., Latariya E.L., Tcelykovskaia O.B., Kurkov A.A., Berest D.G., Leenman E.E., Vinnichuk S.A., Zemlyanoy V.P. Diagnostic difficulties and treatment features of a patient with presacral myelolipoma. Grekov's Bulletin of Surgery. 2025;184(3):95-99. (In Russ.) https://doi.org/10.24884/0042-4625-2025-184-3-95-99