Dieulafoy’s syndrome
A. V. Shabunin,
P. A. Yartsev,
S. A. Tarasov,
M. M. Rogal,
S. O. Aksenova,
A. A. Kanibolotsky,
R. V. Yelokhovsky,
V. A. Moskalenko,
A. M. Shadiev https://doi.org/10.24884/0042-4625-2025-184-6-77-83
Abstract
Dieulafoy’s syndrome (Dieulafoy’s lesion) is an abnormality of vascular development of the submucosal layer of the gastrointestinal tract, with destruction of the covering layers of the epithelium and the absence of a primary ulcer, accompanied by massive bleeding. This paper presents a comprehensive approach in the diagnosis and treatment of Dieulafoy’s syndrome in a young patient. Application of endoscopic, radiological and surgical methods allowed to stabilize the patient’s condition and prevent recurrences. Analysis of literature data shows that in such rare cases of multiple lesions – resection surgery remains the only effective method. The work emphasizes the importance of multidisciplinary approach in the treatment of rare diseases.
About the Authors
A. V. Shabunin
S. P. Botkin Moscow Multidisciplinary Research and Clinical Center
Russian Federation
Competing Interests:
Russian Federation
Shabunin Aleksey V., Dr. of Sci. (Med.), Professor, Academician of the Russian Academy of Sciences, Chief Surgeon and Endoscopist of the Moscow Department of
Healthcare, Director
5, 2nd Botkinsky pr., Moscow, 125284
Competing Interests:
The authors declare no conflict of interest.
P. A. Yartsev
N.V. Sklifosovsky Research Institute for Emergency Care
Russian Federation
Competing Interests:
Russian Federation
Yartsev Petr A., Dr. of Sci. (Med.), Professor, Head of the Department of Emergency Surgery, Endoscopy and Intensive Care
3, Bolshaya Sukharevskaya pl., Moscow, 129090
Competing Interests:
The authors declare no conflict of interest.
S. A. Tarasov
N.V. Sklifosovsky Research Institute for Emergency Care
Russian Federation
Competing Interests:
Russian Federation
Tarasov Sergey A., Cand. of Sci. (Med.), Surgeon, Senior Researcher, Department of Emergency Surgery, Endoscopy, and Intensive Care
3, Bolshaya Sukharevskaya pl., Moscow, 129090
Competing Interests:
The authors declare no conflict of interest.
M. M. Rogal
N.V. Sklifosovsky Research Institute for Emergency Care
Russian Federation
Competing Interests:
Russian Federation
Rogal Mikhail M., Cand. of Sci. (Med.), Surgeon, Research Fellow, Department of Emergency Surgery, Endoscopy, and Intensive Care
3, Bolshaya Sukharevskaya pl., Moscow, 129090
Competing Interests:
The authors declare no conflict of interest.
S. O. Aksenova
N.V. Sklifosovsky Research Institute for Emergency Care
Russian Federation
Competing Interests:
Russian Federation
Aksenova Sofya O., Surgeon
3, Bolshaya Sukharevskaya pl., Moscow, 129090
Competing Interests:
The authors declare no conflict of interest.
A. A. Kanibolotsky
N.V. Sklifosovsky Research Institute for Emergency Care
Russian Federation
Competing Interests:
Russian Federation
Kanibolotsky Alexandr A., Cand. of Sci. (Med.), Head of the Pathology Department
3, Bolshaya Sukharevskaya pl., Moscow, 129090
Competing Interests:
The authors declare no conflict of interest.
R. V. Yelokhovsky
N.V. Sklifosovsky Research Institute for Emergency Care
Russian Federation
Competing Interests:
Russian Federation
Yelokhovsky Roman V., Radiologist, Head of the Department of Radiology
3, Bolshaya Sukharevskaya pl., Moscow, 129090
Competing Interests:
The authors declare no conflict of interest.
V. A. Moskalenko
N.V. Sklifosovsky Research Institute for Emergency Care
Russian Federation
Competing Interests:
Russian Federation
Moskalenko Vladislav A., Doctor of X-ray endovascular diagnostics and treatment, Junior Research Fellow, Department of X-ray Surgical Diagnostic and Treatment Methods
3, Bolshaya Sukharevskaya pl., Moscow, 129090
Competing Interests:
The authors declare no conflict of interest.
A. M. Shadiev
N.V. Sklifosovsky Research Institute for Emergency Care
Russian Federation
Competing Interests:
Russian Federation
Shadiev Artur M., Endoscopist
3, Bolshaya Sukharevskaya pl., Moscow, 129090
Competing Interests:
The authors declare no conflict of interest.
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Review
For citations:
Shabunin A.V., Yartsev P.A., Tarasov S.A., Rogal M.M., Aksenova S.O., Kanibolotsky A.A., Yelokhovsky R.V., Moskalenko V.A., Shadiev A.M. Dieulafoy’s syndrome. Grekov's Bulletin of Surgery. 2025;184(6):77-83. (In Russ.) https://doi.org/10.24884/0042-4625-2025-184-6-77-83
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